Sensorineural hearing loss may be shocking news to patient and his relatives. Understanding is required to help accept the fact, Talk with your doctor, friends, family and person with same problem to support you.
Most patients are benefited by hearing aids but there is limitation of sound-quality and back ground noise that means it works well in quiet environment but some users have trouble enjoying music and listening in a crowded room.
Hearing impaired person takes time to get used to hearing aid. Assistive listening devices, loop system, FM system, and telephone and mobile amplifying devices help in clarity of sound and music.
Working together to hear better may be tough on everyone. It will take time for hearing impaired person to get used to watching people as they talk and for people to get used to speaking louder and clear.
Be patient and continue to work together.
Treatment and devices for hearing loss
Train your new way of hearing (getting used to hearing aid)
Help from family and friends
What treatments and devices can help?
- Hearing aids are tiny instruments which make sounds louder.
Quality of hearing aid is of utmost importance and it takes few days to adjust but eventually initial chaotic sound disappear and person is able to appreciate the difference.
- Personal listening systems help you hear what you want to hear while eliminating other noises around you. Auditory training systems and loop systems make it easier to hear in a crowded room. FM systems and personal amplifiers are better for one-on-one conversations. Improving FM (frequency modulation) boosts the performance of hearing aid.
- TV listening systems help you listen to the television or the radio without being disturbed by other noises around you. These systems can be used with or without hearing aids.
- Direct audio input hearing aids are hearing aids that can be plugged into TVs, stereos, microphones, auditory trainers, and personal FM systems to help you hear better.
- Telephone and mobile amplifying devices. If your hearing aid has a “T” switch, you can use a phone with an amplifying coil (T-coil) or mobile phone with a loop set. It allows you to listen at a comfortable volume and helps lessen background noise. Special type of telephone receiver and other devices are also available to make sounds louder on the phone.
- Assistive listening systems. Many auditoriums, movie theaters, churches, synagogues, and other public places are equipped with special sound systems for people with hearing loss. These systems send sounds directly to your ears to help you hear better.
- Lip reading or speech reading is another option.
How to train your new way of hearing (getting used to hearing aid)
Hearing aid is not same as natural hearing but with few weeks of regular use person usually adapt to it. A period of adjustment is required as the brain gets used to this new way of dealing with sound.
I. At first, wear the hearing aids in your home environment.
- Wear the hearing aids only as long as you are comfortable wearing them.
- Read something aloud to yourself. Try to listen to soft noises, such as rustling paper, tape water, jingling your keys, etc.
- Make a brief phone call
- Have a conversation with a friend or relative in calm, quiet surroundings.
- Watch a television show or listen to a radio programme in quiet surroundings.
II. Have a conversation in a loud environment. It may take a few days or a few weeks to adjust.
- Even people with normal hearing do not hear every word.
- In loud hearing situations, even people without hearing loss need to make an effort in order to hear what they need to hear and ignore the unwanted noise.
III. Gradually increase the hours of wearing hearing aids over 15-20 days.
IV. Gradually extend the number of persons with whom you speak.
V. Be patient and focused.
How friends and family can help the hearing impaired?
- Know and talk about his hearing loss.
- Face the person with hearing loss and maintain eye contact when you talk. Your face and expressions may help you to understand them better.
- Speak louder, but do not shout. Just talk more clearly and slowly.
- Turn off the TV or the radio if it is not required.
- Be aware of noise around you that can make his hearing more difficult, like vacuum cleaner, washing machine or loud music Shorten the distance between you and listener in noisy surroundings.
- Be patient
Hearing loss can range from a mild impairment to profound loss. Conductive hearing loss is largely preventable and can be managed by medicine/surgery. Sensor neural hearing loss may need fitting with hearing aids.
Early identification of hearing loss in newborn and young children is of critical as he develops language and speech by hearing to his surroundings.
In general neonates and infants could be tested by BERA, children in the age group of 2 – 3 yrs could be screened using free – field audiometry, children above 4 yrs could be conditioned and then a audiometry can be performed to test hearing impairment.
Babies should be screened for hearing at birth especially high risk ones.
Child with mild hearing loss is generally labeled as inattentive or slow learner. Hearing should be tested as child grows at any time on slightest suspicion of hearing deficit by Parents, care givers, teachers and family doctors.
Screening for hearing has been done for many years but still does not detect hearing impairment as early as desirable. Mother’s instinct for her child is usually correct even at early age and should not be neglected.
The type of tests used to identify hearing loss depend on the age of the child, and include:
* Behavioural observation audiometry (BOA) – for babies less than seven months of age.
It consists of making noises, such as shaking a rattle close to ear, and then observing the baby’s response.
* Distraction method – it is formalized method of behavioral observation audiometry for children 7-19 months.
Infant sits on mother’s lap and one tester standing in front uses toys to raise attention. Other tester behind the child presents signals like shaking a rattle, or drum beat. First tester observes the child’s response. Response may be head turn, eye turn, frowning, sucking etc. After each response the signal intensity used to elicit a response is measured.
* Visual reinforcement orientation (VRA) – useful for children 7-30 months of age. The baby is taught to move their head towards sound by pairing it with an interesting visual stimulus, located in the direction of the speaker. Their response to different sounds can then be measured. Test is done in sound proof room with speaker and headphone. The ears can be tested individually if the baby tolerates headphones.
* Performance audiometry test – older children are taught to respond to sounds by a performing a simple action or playing a game, such as dropping a marble when they hear the sound.
* Oto-acoustic emission – certain sounds generated by the inner ear can be recorded to check the function of the tiny hair cells in the cochlea.
* Auditory brainstem response testing – to check the electrical activity in the brain in response to a sound. Electrodes are placed on the head to measure the brain waves. It is most popular test for neonatal hearing assessment and for detection of hearing loss.
* Transtympanic Electrocochleography – to check the cochlea for signs of electrical activity in response to sound. It is better indicator of hearing threshold than any other auditory evoked response in children. An electrode is threaded through the eardrum to touch the cochlea and it requires general aneasthesia in children.
* Impedance audiometry or Tympanometry – a probe which snugly fits into the ear and air is pumped into the ear canal. Neonates and young infants may be examined so long as the probe tone is 660 Hz and not 220 Hz. Stapedius reflex are used to assess middle ear disfunction. Impedance audiometry is not an alternative to behavioral audiometry.t
Click here to see Anatomy of ear and hearing, animation on medindia.net
Ear is divided into three parts-
- Outer ear (pinna and external auditory canal)
- Middle ear (ear drum, ear ossicles)
- Inner ear (cochlea,semicircular canals and vestibule)
Outer ear protects ear drum and sends sound to the middle ear and protect ear drum. Outer 1/3rd of canal contains ceruminous glands which secret wax .
Middle ear is an air filled cavity separated from external ear by ear drum and connects to nasopharynx by Eustachian tube. Middle ear contain three small movable bones (ossicles) malleus, incus and stapes which converts sound waves into mechanical vibrations.
Inner ear contains cochlea (for hearing ) and semicircular canals & vestibule (for balance ).
First three years of life are critical for a child to develop speech and language skill. For effective language and communication skill development child need to hear normally. If any hearing impairment is there it should be managed at the earliest.
With modern technologies like Brain-stem evoked response audiometry it is possible to identify hearing-loss within days of birth.
There are certain criteria which needs to pay attention and newborn should be subjected to hearing evaluation:–
1. Parental concern about hearing levels or speech delay in their child
2. Family history of hearing loss
3. History of in-utero (cytomegalovirus, rubella or syphilis) or post natal infections (meningitis)
4. Low birth weight babies
5. Hyper Bilirubinemia
6. Cranio facial deformities or certain syndromes
7. Head injury
8. Recurrent or Persistent otitis media with effusion
9. Exposure to ototoxic drugs
Tests of hearing:-
- Finger friction test
- Watch test
- Speech test; whisper and conversational speech
- Tuning fork tests
- Pure-tone audiometry
- Impedance audiometry / tympanometry
- Brain-stem evoked response audiometry
Finger friction test, watch test, clinical speech test and tuning fork tests are often used for hearing screening or bed side testing.
Tuning-forks test :–
256, 512 and 1024 Hz frequency, vibrating tuning forks are placed in front of ear (to test air conduction), behind the ear and over the forehead (to test bone conduction; here sound is directly transmitted to the cochlea) to get an idea of hearing, and degree & type of hearing impairment if any.
The tuning fork should be struck against elbow or knee, and not against a table or desk to avoid undesirable harmonics.
Result of tuning fork test:
Rinne test described as being positive (normal/conductive deafess) or negative (sensorineural deafness),
Weber test described as being central (normal) or lateralized to one ear (same side conductive loss or other side sensorineural loss; interpreted along with Rinne test)
Schwabach’s test where patients bone conduction is compared with that of examiner’s..
Audiometer is an electronic device which produces pure-tones.
Person has to put on headphones and then listen for some different tones from low pitch to high pitch. Person has to push a button or raise hand when he hears each tone.
Hearing is measured at different frequencies from (250 Hz to 8,000 Hz). Results in decibels are charted in the form of graph called audiogram.
This procedure is called Pure-tone Audiometry.
It is a subjective test of hearing and cooperation and understanding of patient is of utmost importance.
Audiometry is required: –
1. To know degree and type of hearing loss.
2. To keep record and for medico-legal purposes.
3. Before prescribing a hearing-aid.
Figure 1: An audiogram of an ear with normal hearing
Result interpretation; Reading Audiogram-
Normal hearing: less than 15-25 decibels
Minimal loss: 16 to 25 decibel loss
Mild loss: 26-40 decibel loss
Moderate loss: 41-55 decibel loss
Moderately severe Loss – 56 to 70 decibel loss
Severe loss: 71 to 90 decibel loss
Profound: 91 decibel loss and above
To know the type of hearing loss bone conduction is tested, If hearing is better by bone conduction a conductive loss is present.
Patient’s ability to hear and understand speech is measured.
Certain number of words presented via head phones or free field loud speakers, and person asked to repeat the words.
Speech reception threshold is minimum intensity at which a person is able to repeat at least 50% of words correctly. Here a set of two syllable words with equal stress on each syllable (spondee words) are used.
Speech discrimination score is percentage of words heard correctly when phonetically balanced words at 30 to 40 decibel above the person’s hearing threshold are presented.
A score of 90 – 100% is considered excellent, 80 – 89% is good, 70 – 79% is fair, 60 – 69% is poor, <50% is considered very poor.
Tympanometry or Impedance audiometry –
Objective test of hearing; particularly useful to test hearing in infant and child, to know patency of Eustachian tube, and to know condition of middle ear like presence of fluid or fixation (as in otosclerosis) or dislocation of ossicles.
Ossicles are 3 small bones present in middle ear namely malleus, incus and stapes.
Equipment consists of a probe which snugly fits into external ear canal.
Tymanometry is the dynamic measurement of middle ear pressure through measuring mobility of the tympanic membrane. The resultant changes in air pressure variation are plotted on a graph called tympanogram.
Acoustic reflex testing consists of response contraction of subjecting the ear to a loud sound a rough method of evaluating hearing.
Interpretation of tympanogram:-
Fig-2: Different types of tympanograms (pic taken from http://ivertigo.net/graphics/v14.gif)
The shape of the tympanogram suggests how the eardrum is functioning.
1. Normal eardrum movement is shows a well-formed peak, where height of the peak indicates the amount of eardrum compliance, (type A).
2. A flat line indicates little or no eardrum movement. This type of tympanogram (type B)is commonly seen when fluid is present behind the eardrum or when there is a hole or perforation in the eardrum .
3. A peak to the left of the normal pressure range (type c) means adequate eardrum movement with negative middle ear pressure, seen in persistent cold or initial phase of fluid accumulation or recovery phase of fluid accumulation.
Reduced mobility with normal middle ear pressure (type As) is seen in otosclerosis.
Normal middle ear pressure with hyper-mobility (type Ad) is seen in disruption of ossicular chain.
Brain stem evoked response audiometry (BERA): –
Auditory brain stem response (ABR) audiometry, Brainstem auditory evoked response audiometry (BAER)
It is a test of neurological activity of auditory nerve and brain stem in response to auditory stimuli.
Electrodes are placed on scalp and ear lobe and patient is asked to relax and remain still .
Clinical uses of BERA
1. It is an effective screening tool for evaluating cases of deafness due to retro cochlear pathology i.e. (Acoustic schwannoma).
2. Used in screening newborns for deafness
3. Used for intra-operative monitoring of central and peripheral nervous system
4. Monitoring patients in intensive care units
5. Diagnosing suspected demyelinated disorders (multiple sclerosis)